{"id":7572,"date":"2021-07-15T09:24:44","date_gmt":"2021-07-15T12:24:44","guid":{"rendered":"https:\/\/med.estrategiaeducacional.com.br\/blog\/?p=7572"},"modified":"2022-09-12T20:04:45","modified_gmt":"2022-09-12T23:04:45","slug":"siringomielia","status":"publish","type":"post","link":"https:\/\/med.estrategia.com\/portal\/conteudos-gratis\/doencas\/siringomielia\/","title":{"rendered":"Siringomielia: causas, sintomas e muito mais!"},"content":{"rendered":"<p>Quer descobrir tudo sobre a siringomielia? O Estrat&eacute;gia MED separou para voc&ecirc; as principais informa&ccedil;&otilde;es sobre o assunto. Acompanhe este texto e descubra!<div id=\"ez-toc-container\" class=\"ez-toc-v2_0_79_2 counter-hierarchy ez-toc-counter ez-toc-transparent ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\"><p class=\"ez-toc-title\" style=\"cursor:inherit\">Navegue pelo conte\u00fado<\/p>\n<\/div><nav><ul class='ez-toc-list ez-toc-list-level-1 ' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/med.estrategia.com\/portal\/conteudos-gratis\/doencas\/siringomielia\/#O-que-e-siringomielia\" >O que &eacute; siringomielia?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/med.estrategia.com\/portal\/conteudos-gratis\/doencas\/siringomielia\/#Quais-as-causas-da-siringomielia\" >Quais as causas da siringomielia?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/med.estrategia.com\/portal\/conteudos-gratis\/doencas\/siringomielia\/#Sintomas-de-siringomielia\" >Sintomas de siringomielia<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/med.estrategia.com\/portal\/conteudos-gratis\/doencas\/siringomielia\/#Diagnostico\" >Diagn&oacute;stico<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/med.estrategia.com\/portal\/conteudos-gratis\/doencas\/siringomielia\/#Tratamento\" >Tratamento<\/a><\/li><\/ul><\/nav><\/div>\n<h2 class=\"wp-block-heading\" id=\"h-o-que-e-siringomielia\"><span class=\"ez-toc-section\" id=\"O-que-e-siringomielia\"><\/span>O que &eacute; siringomielia?<span class=\"ez-toc-section-end\"><\/span><\/h2><p>A <strong>siringomielia <\/strong>&eacute; a presen&ccedil;a de uma <strong>cavidade <\/strong>&ndash; a siringe &ndash; <strong>com cole&ccedil;&atilde;o l&iacute;quida na medula espinhal<\/strong>, que pode se expandir e causar les&otilde;es nervosas. &Eacute; uma <strong>doen&ccedil;a rara<\/strong>, com preval&ecirc;ncia de, aproximadamente, um caso para cada 12.500 pessoas.<\/p><h2 class=\"wp-block-heading\" id=\"h-quais-as-causas-da-siringomielia\"><span class=\"ez-toc-section\" id=\"Quais-as-causas-da-siringomielia\"><\/span>Quais as causas da siringomielia?<span class=\"ez-toc-section-end\"><\/span><\/h2><figure class=\"wp-block-image\"><img decoding=\"async\" src=\"https:\/\/lh3.googleusercontent.com\/hhQEK4gANuETN9_QTESQ7uAY0Kbj2MMCp3y_gkDCj3hr-iv2dh3nmXs68GIBKJb2ynP9sTQpyUMGevoigLE9-kozAusKOF0DfFkRPoXH58rGotUxaKWVEh2HGCEjE62YOnkEfaIi\" alt=\"Quais as causas da siringomielia?\"><\/figure><p>Na maioria dos casos, a siringomielia &eacute; <strong>cong&ecirc;nita <\/strong>e associada a uma <strong>malforma&ccedil;&atilde;o<\/strong>, denominada <strong>Arnold-Chiari tipo 1<\/strong>, que envolve o cr&acirc;nio. Essa condi&ccedil;&atilde;o promove uma <strong>redu&ccedil;&atilde;o de fluxo do l&iacute;quido cefalorraquidiano<\/strong>, o que for&ccedil;a sua entrada para o canal medular, formando a siringe. Nesse caso, as siringomielias est&atilde;o presentes, principalmente, na <strong>por&ccedil;&atilde;o cervical da medula<\/strong>.<\/p><p>Outras causas poss&iacute;veis s&atilde;o o <strong>trauma de medula espinhal<\/strong>, <strong>aracnoidite <\/strong>e <strong>tumores medulares<\/strong>. Essas situa&ccedil;&otilde;es podem levar &agrave; cavita&ccedil;&atilde;o da estrutura nervosa e entrada de liquor nesse espa&ccedil;o. Nessas hip&oacute;teses, as siringes podem estar presentes em <strong>qualquer por&ccedil;&atilde;o da medula<\/strong>.&nbsp;<\/p><h2 class=\"wp-block-heading\" id=\"h-sintomas-de-siringomielia\"><span class=\"ez-toc-section\" id=\"Sintomas-de-siringomielia\"><\/span>Sintomas de siringomielia<span class=\"ez-toc-section-end\"><\/span><\/h2><p>Tal condi&ccedil;&atilde;o pode ser <strong>assintom&aacute;tica <\/strong>e identificada de maneira incidental. Quando h&aacute; <strong>sintomas<\/strong>, geralmente surgem entre a <strong>segunda e quarta d&eacute;cadas de vida<\/strong>, com m&eacute;dia de 30 anos de idade e dependem principalmente da topografia da les&atilde;o. S&atilde;o eles:<\/p><ol class=\"wp-block-list\"><li><strong>Dissocia&ccedil;&atilde;o anest&eacute;sica<\/strong>: perda de sensibilidade de dor e temperatura e preserva&ccedil;&atilde;o do tato e propriocep&ccedil;&atilde;o;<\/li><li><strong>Paresia <\/strong>progressiva de membros;<\/li><li><strong>Atrofia <\/strong>muscular; e<\/li><li>Altera&ccedil;&otilde;es na <strong>propriocep&ccedil;&atilde;o <\/strong>e <strong>sensibilidade vibrat&oacute;ria<\/strong>.<\/li><\/ol><h2 class=\"wp-block-heading\" id=\"h-diagnostico\"><span class=\"ez-toc-section\" id=\"Diagnostico\"><\/span>Diagn&oacute;stico<span class=\"ez-toc-section-end\"><\/span><\/h2><p>O diagn&oacute;stico &eacute; feito com base na <strong>anamnese compat&iacute;vel <\/strong>com a condi&ccedil;&atilde;o e <strong>exame neurol&oacute;gico completo<\/strong>, com o objetivo de topografar a les&atilde;o e excluir outras poss&iacute;veis causas. Al&eacute;m disso, como exame complementar, &eacute; necess&aacute;rio pedir <strong><a href=\"https:\/\/med.estrategia.com\/portal\/aluno-de-medicina\/dicas-de-estudo\/ressonancia-magnetica\/\" target=\"_blank\">resson&acirc;ncia magn&eacute;tica<\/a><\/strong> da regi&atilde;o acometida pela siringomielia, para confirmar o diagn&oacute;stico, avaliar a sua extens&atilde;o e definir o progn&oacute;stico e a conduta terap&ecirc;utica.&nbsp;<\/p><h2 class=\"wp-block-heading\" id=\"h-tratamento\"><span class=\"ez-toc-section\" id=\"Tratamento\"><\/span>Tratamento<span class=\"ez-toc-section-end\"><\/span><\/h2><p>Quando o achado &eacute; incidental e a patologia n&atilde;o causa nenhum dist&uacute;rbio neurol&oacute;gico no paciente, a <strong>conduta <\/strong>&eacute; meramente <strong>expectante<\/strong>, com acompanhamento cl&iacute;nico da evolu&ccedil;&atilde;o da condi&ccedil;&atilde;o. Entretanto, quando h&aacute; presen&ccedil;a de <strong>sintomas <\/strong>comprometendo o bom funcionamento da medula, &eacute; fundamental a realiza&ccedil;&atilde;o de <strong><a href=\"https:\/\/med.estrategia.com\/portal\/profissoes-da-medicina\/neurocirurgia\/\" target=\"_blank\">neurocirurgia <\/a><\/strong>para corre&ccedil;&atilde;o da siringomielia.&nbsp;<\/p><p>Quando a doen&ccedil;a se associa &agrave; <strong>malforma&ccedil;&atilde;o de Arnold-Chiari tipo 1<\/strong>, o procedimento de elei&ccedil;&atilde;o &eacute; a <strong>descompress&atilde;o da fossa posterior<\/strong>, com a realiza&ccedil;&atilde;o de craniectomia suboccipital e laminectomia de C1. Se houver <strong>tumor <\/strong>levando &agrave; forma&ccedil;&atilde;o de siringes, faz-se necess&aacute;ria a <strong>ressec&ccedil;&atilde;o da massa<\/strong>. Por&eacute;m, algumas vezes, a &uacute;nica alternativa terap&ecirc;utica &eacute; <strong>drenar a siringe para o espa&ccedil;o pleural<\/strong>.<\/p><p>Gostou do conte&uacute;do que o Estrat&eacute;gia MED trouxe para voc&ecirc;? Ent&atilde;o n&atilde;o deixe de aproveitar as outras <strong>op&ccedil;&otilde;es para estudo<\/strong> que preparamos para voc&ecirc;! Se voc&ecirc; vai se preparar para as principais e mais concorridas provas de Resid&ecirc;ncia M&eacute;dica do Brasil, ent&atilde;o o <a href=\"https:\/\/med.estrategiaeducacional.com.br\/#plans-session\" target=\"_blank\"><strong>Curso Extensivo<\/strong> <\/a>do Estrat&eacute;gia MED &eacute; o seu principal aliado.&nbsp;<\/p><p>Na <strong>plataforma <\/strong>do Estrat&eacute;gia MED, h&aacute; <strong>videoaulas <\/strong>elaboradas especialmente para a prepara&ccedil;&atilde;o para a<strong> <\/strong>prova de Resid&ecirc;ncia M&eacute;dica, <strong>material <\/strong>completo e constantemente atualizado, banco com milhares de <strong>quest&otilde;es resolvidas<\/strong>, possibilidade de montar <strong>simulados <\/strong>e de estudar<strong> onde e quando quiser<\/strong>. Se interessou? Clique no banner abaixo e saiba mais.&nbsp;<\/p><p><\/p><p><strong><a id=\"cta\" class=\"cta-imagem\" href=\"https:\/\/med.estrategia.com\/cursos\/extensivo-de-residncia-mdica\/\" target=\"blank\">\n                <img decoding=\"async\" width=\"100%\" src=\"https:\/\/med.estrategia.com\/portal\/wp-content\/uploads\/2025\/08\/extensivo_rm.jpg\" alt=\"Extensivo RM\" title=\"extensivo_rm\">\n        <\/a><\/strong><\/p><\/p>\n","protected":false},"excerpt":{"rendered":"Quer descobrir tudo sobre a siringomielia? O Estrat&eacute;gia MED separou para voc&ecirc; as principais informa&ccedil;&otilde;es sobre o assunto.&hellip;\n","protected":false},"author":15,"featured_media":7573,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"wl_entities_gutenberg":"","footnotes":""},"categories":[304],"tags":[58],"wl_entity_type":[199],"class_list":{"0":"post-7572","1":"post","2":"type-post","3":"status-publish","4":"format-standard","5":"has-post-thumbnail","7":"category-doencas","8":"tag-neurologia","9":"wl_entity_type-article"},"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.6 (Yoast SEO v26.6) - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Siringomielia: causas, sintomas e muito mais!<\/title>\n<meta name=\"description\" content=\"Quer saber tudo sobre a siringomielia, o que \u00e9, causas, sintomas e tratamento? 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